Skull vault hemangioma

Skull vault hemangiomas (SVH), or hemangiomas of the calvaria, are benign slow-growing vascular neoplasms affecting the skull diploe in any location. 

Please refer to the article on intraosseous hemangiomas for a general discussion of that entity. 

The calvaria is the second most prevalent site for intraosseous hemangiomas, particularly the frontal and parietal bones 1. It represents 10% of benign neoplasms of the skull 4 and 0.2% of all osseous tumors 2. Commonly occurs in women in the 4th-5th decades of life with a 3:1 female-male ratio 4.

These tumors are slow-growing and are generally asymptomatic, unless when palpable due to a lump produced by an expansion of the outer table 3

As an intraosseous hemangioma, skull vault hemangiomas are classified as venous, cavernous, or capillary type, according to their predominant vascular network. Histologically, it demonstrates hamartomatous vascular tissue within endothelium, but may also contain fat, smooth muscle, fibrous tissue, and thrombus 1-3.

Lytic lesion with a sclerotic rim (usually with a honeycomb- or sunburst-like appearance).

Usually presents as an expansile bone lesion with thin borders and a characteristic sunburst pattern of trabecular thickening radiating from a common center. Erosions of both internal or external plates can occur and may be associated with internal or external tumor expansion. Sometimes, bony trabeculae can grow beyond the cortical bone, and simulate an aggressive pseudo-"hair-on-end" periosteal reaction 4.

DSA is important for the surgical planning of smaller lesions and embolization of larger ones.  

Signal intensity is somewhat variable, depending largely on the amount of fat content 4

  • T1: typically hyperintense, though atypical T1 hypointense forms are not rare. 
  • T2/FLAIR: hyperintense signal 
  • T1 C+ (Gd): homogeneous enhancement is often present

​Treatment usually not necessary. Rare indications include: mass effect, hemorrhage control, and aesthetic improvement. Treatment options are:

  • radiation therapy
  • embolization to reduce intraoperative blood loss
  • surgical resection
  • intralesional ethanol injection

Article information

rID: 34187
Synonyms or Alternate Spellings:
  • Haemangiomas of the calvaria
  • Skull vault haemangiomas
  • Skull vault hemangioma
  • Skull vault hemangiomas
  • Cranial vault haemangioma
  • Cranial vault haemangiomas
  • Cranial vault hemangioma
  • Cranial vault hemangiomas

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